Ruptured Sinus of Valsalva Aneurysm Associated with Situs Ambiguus, Isolated Levocardia, and Polysplenia

Authors

Safieh Golestaneh MD, Baystate HealthFollow
Mohammad Amin Kashef MD, Baystate HealthFollow
William Hiser MD, Baystate HealthFollow
Amir Lotfi, Baystate HealthFollow
Timothy Egan MD, Baystate HealthFollow

Author Department

Medicine; Cardiology

Document Type

Article, Peer-reviewed

Publication Date

12-2017

Abstract

Aneurysm of the sinus of Valsalva, a rare cardiac condition, results from dilation of an aortic sinus. Sudden aneurysm rupture can trigger rapidly progressive heart failure. We discuss the case of a 57-year-old woman with situs ambiguus, isolated levocardia, and polysplenia who presented with acute-onset heart failure. Transesophageal echocardiograms revealed an aneurysm of the right coronary sinus of Valsalva that had ruptured into the right atrial cavity. The patient underwent successful surgical repair. To our knowledge, this is the first report of a sinus of Valsalva aneurysm in a patient with this combination of congenital abnormalities. We briefly review the association between congenital heart disease, situs ambiguus, and ciliary dysfunction.

Recommended Citation

Golestaneh S, Kashef MA, Hiser WL, Lotfi AS, Egan TG. Ruptured Sinus of Valsalva Aneurysm Associated with Situs Ambiguus, Isolated Levocardia, and Polysplenia. Tex Heart Inst J. 2017 Dec 19;44(6):416-419.

PMID

29276443